Cronkhite-Canada syndrome: a new case report of this enigmatic and infrequent disease.
نویسندگان
چکیده
The Cronkhite-Canada syndrome (CCS) is an infrequent disease, non-inherited, characterized by a gastrointestinal non-adenomatous polyposis, chronic diarrhea, low blood proteins, malnutrition and skin and nail alterations (1-6). Etiopathogeny is unknown, there is no effective treatment with a scientific base and, although cases with response to empiric treatments have been described, prognosis is usually poor. We do not know if with an early diagnosis, the prognosis could be better. We expose a new case of this enigmatic and infrequent disease, with no medical treatment response, in order to remind it, improving the casuistry and the available information about it, and promoting, with a higher knowledge and diffusion, an earlier treatment.
منابع مشابه
Cronkhite–Canada syndrome six decades on: the many faces of an enigmatic disease.
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عنوان ژورنال:
- Revista espanola de enfermedades digestivas : organo oficial de la Sociedad Espanola de Patologia Digestiva
دوره 102 3 شماره
صفحات -
تاریخ انتشار 2010